Clinical Profile and Quality of Life of Adult Patients After the Fontan Procedure.

Pediatric cardiology

PubMedID: 25828147

Bordin G, Padalino MA, Perentaler S, Castaldi B, Maschietto N, Michieli P, Crepaz R, Frigo AC, Vida VL, Milanesi O. Clinical Profile and Quality of Life of Adult Patients After the Fontan Procedure. Pediatr Cardiol. 2015;.
Increasingly, more patients with univentricular heart reach adulthood. Therefore, long-term psychological features are an important concern. THE AIM
of this study was to evaluate the clinical and psychological profile of post-Fontan adult patients and to identify the most significant determinants of quality of life.The aim of this study was to evaluate the clinical and psychological profile of post-Fontan adult patients and to identify the most significant determinants of quality of life. In this retrospective cross-sectional study, we reviewed the surgical and medical history of post-Fontan adult patients.

PATIENTS
underwent a 24-h electrocardiogram, echocardiography and exercise testing.Patients underwent a 24-h electrocardiogram, echocardiography and exercise testing. Self-report questionnaires were used to assess the Work Ability Index, quality of life (Satisfaction with Life Scale), perceived health status (SF-36 questionnaire), coping strategies (Brief Cope questionnaire) and presence of mood disorders (Hospital Anxiety and Depression Scale). Thirty-nine patients aged between 18 and 48 years (mean 27. 5 years) were enrolled. The mean follow-up was 21. 5 years. Most patients were unmarried (82. 9 %), had a high school diploma (62. 9 %) and were employed (62. 9 %). Twenty-nine patients (82. 3 %) had at least one long-term complication. The median single ventricle ejection fraction was 57 %, and the median maximal oxygen consumption was 26. 8 ml/min/kg. This population tended to be anxious and to use adaptive coping strategies. Quality of life was perceived as excellent or good in 57. 2 % of cases and was not related to either cardiac function or exercise capacity. Both quality of life and SF-36 domains were related to the Work Ability Index. This cohort of post-Fontan adult patients enjoyed a good quality of life irrespective of disease severity.