Extrarenal testicular Wilms' tumor in a 3-year-old child.

Pediatric surgery international

PubMedID: 23794024

Morandi A, Fagnani AM, Runza L, Farris G, Zanini A, Parolini F, Bassi G, Gentilino V, Macchini F, Arnoldi R, Leva E. Extrarenal testicular Wilms' tumor in a 3-year-old child. Pediatr Surg Int. 2013;29(9):961-4.
We report an extremely rare case of extrarenal testicular Wilms' tumor in a 3-year-old boy with intrabdominal undescended left testis. The patient was admitted because of pain and vomiting, with evidence of a huge abdominal mass. At surgery a large tumor arising from the intrabdominal testis was found. Histology showed the classical triphasic Wilms' tumor elements: epithelial, mesenchymal and blastemal areas. Extrarenal Wilms' tumors account for only 3 % of all Wilms' tumors and just ~100 cases have been reported in literature. Testicular origin is anecdotic. We present histomorphological, histogenetic, clinical, diagnostic, prognostic and therapeutic features of this rare tumor.